Case Report

Macrodystrophia lipomatosa – MR imaging of a rare congenital anomaly: review of 3 cases

Pallavi Aga, Umesh C Parashari, Anit Parihar, Ragini Singh, Neera Kohli, Rajesh Yadav
South African Journal of Radiology | Vol 14, No 4 | a456 | DOI: https://doi.org/10.4102/sajr.v14i4.456 | © 2010 Pallavi Aga, Umesh C Parashari, Anit Parihar, Ragini Singh, Neera Kohli, Rajesh Yadav | This work is licensed under CC Attribution 4.0
Submitted: 24 February 2010 | Published: 07 December 2010

About the author(s)

Pallavi Aga,, India
Umesh C Parashari,, India
Anit Parihar,, India
Ragini Singh,, India
Neera Kohli,, India
Rajesh Yadav,, India

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Abstract

Macrodystrophia lipomatosa (MDL) results from progressive overgrowth of all the mesenchymal elements, with a disproportionate increase in fibro-adipose tissue. This rare congenital abnormality occurs most frequently in the distribution of the median nerve in the upper, and medial plantar nerve in the lower, extremity.

Excess of unencapsulated fibro-adipose tissue on magnetic resonance imaging (MRI) is virtually diagnostic and can differentiate this entity from other diseases with similar presentations. Involvement of the ulnar aspect of the hand, though rare, has been described; however, the lateral aspect of the foot as seen in our second case has not been reported, to the best of our knowledge.

Keywords

MRI ; Macrodystrophia lipomatosa

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