Case Report

Imaging features of a rare case of scapuloiliac dysostosis (Kosenow syndrome) in an ambulatory child

John Joseph, Harish Narayanan, Jacob Varghese, Harish Babu, A Praveen
South African Journal of Radiology | Vol 15, No 1 | a338 | DOI: https://doi.org/10.4102/sajr.v15i1.338 | © 2011 John Joseph, Harish Narayanan, Jacob Varghese, Harish Babu, A Praveen | This work is licensed under CC Attribution 4.0
Submitted: 24 February 2011 | Published: 21 February 2011

About the author(s)

John Joseph,, India
Harish Narayanan,, India
Jacob Varghese,, India
Harish Babu,, India
A Praveen,, India

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Abstract

Scapuloiliac dysostosis, also known as pelvis-shoulder dysplasia and Kosenow syndrome, is a rare skeletal dysplasia described first by Kosenow et al. in 1970. The main components of the syndrome are varying degrees of bilateral iliac and scapular hypoplasia. Various other skeletal abnormalities including exaggerated lumbar lordosis, and clavicular, vertebral, rib and long bone anomalies and extra-skeletal abnormalities, most commonly those of eye and ear, have also been reported. We report the plain radiography, CT and MRI findings of an interesting case of the syndrome.

Keywords

Scapuloillac dysostosis, Kosenow syndrome, pelvis-shoulder dysplasia, iliac agenesis, scapular hypoplasia.

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