Case Report

Tuberous sclerosis complex: The critical role of the interventional radiologist in management

Puneet Garg, Anuradha Sharma, Heena Rajani, Apratim R. Choudhary, Rajkumar Meena
South African Journal of Radiology | Vol 25, No 1 | a2034 | DOI: https://doi.org/10.4102/sajr.v25i1.2034 | © 2021 Puneet Garg, Anuradha Sharma, Heena Rajani, Apratim R. Choudhary, Rajkumar Meena | This work is licensed under CC Attribution 4.0
Submitted: 25 October 2020 | Published: 30 March 2021

About the author(s)

Puneet Garg, Department of Radiology, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India
Anuradha Sharma, Department of Radiology, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India
Heena Rajani, Department of Radiology, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India
Apratim R. Choudhary, Department of Radiology, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India
Rajkumar Meena, Department of Radiology, Vardhman Mahavir Medical College and Safdarjung Hospital, New Delhi, India

Abstract

Tuberous sclerosis complex (TSC) is an autosomal dominant neurocutaneous syndrome that is characterised by hamartomas in multiple organs, the characteristic imaging features of which are illustrated in this case report. Angiomyolipoma (AML) is the most common renal manifestation of TSC, which may present with life-threatening haemorrhage at the time of diagnosis. Interventional management with selective renal embolisation is currently the treatment of choice for the safe and effective management of ruptured renal AML.


Keywords

tuberous sclerosis complex; angiomyolipoma; selective renal embolisation; hamartomas; ruptured angiomyolipoma; renal haemorrhage

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