Pulmonary arteriovenous malformations (AVM) are rare causes of a cardiac murmur in the paediatric population. They are caused by abnormal communications between pulmonary arteries and veins that are most commonly congenital in nature. Although these lesions are fairly uncommon, they are an important differential diagnosis to consider in patients with common pulmonary problems such as hypoxaemia and/or a pulmonary nodule(s). This report illustrates the clinical presentation, radiological features and pathological findings in an eight-month-old boy.

fistula; arteriovenous; congenital; trisorny 21