Case Report

Dyke–Davidoff–Masson syndrome with crossed cerebellar atrophy

Sanjay M. Khaladkar, Shishir Chauhan, Abhijit M. Patil, Siddappa G. Gandage, Surbhi Chauhan Kalra
South African Journal of Radiology | Vol 21, No 1 | a1207 | DOI: https://doi.org/10.4102/sajr.v21i1.1207 | © 2017 Sanjay M. Khaladkar, Shishir Chauhan, Abhijit M. Patil, Siddappa G. Gandage, Surbhi Chauhan Kalra | This work is licensed under CC Attribution 4.0
Submitted: 27 April 2017 | Published: 26 September 2017

About the author(s)

Sanjay M. Khaladkar, Department of Radiology, Dr. D.Y. Patil Medical College, Hospital & Research Centre, Dr. D.Y. Patil Vidyapeeth, India
Shishir Chauhan, Department of Radiology, Dr. D.Y. Patil Medical College, Hospital & Research Centre, Dr. D.Y. Patil Vidyapeeth, India
Abhijit M. Patil, Department of Radiology, Dr. D.Y. Patil Medical College, Hospital & Research Centre, Dr. D.Y. Patil Vidyapeeth, India
Siddappa G. Gandage, Department of Radiology, Dr. D.Y. Patil Medical College, Hospital & Research Centre, Dr. D.Y. Patil Vidyapeeth, India
Surbhi Chauhan Kalra, Department of Radiology, Dr. D.Y. Patil Medical College, Hospital & Research Centre, Dr. D.Y. Patil Vidyapeeth, India

Abstract

Dyke–Davidoff–Masson syndrome is a rare condition with classical, clinical and radiological changes – mental retardation, hemiparesis, facial asymmetry, seizures and cerebral hemiatrophy with calvarial changes. Contralateral cerebellar atrophy is rare and occurs if insult occurs after 1 month of age. We report a case of a 6-year-old female child presenting with right-sided hemiparesis, convulsions and left cerebral hemiatrophy with an old infarct in left middle cerebral artery (MCA) territory, ipsilateral calvarial thickening and right (crossed) cerebellar atrophy.

Keywords

Dyke-Davidoff-Masson Syndrome (DDMS); Cerebellar atrophy; diaschisis; Magnetic Resonance Imaging( MRI )

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Crossref Citations

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